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Advisor(s)
Abstract(s)
A Leiomiomatose Peritoneal Disseminada (LPD) é uma doença rara, frequentemente assintomática, definindo-se como a ocorrência
de múltiplas lesões tumorais peritoneais ou subperitoneais traduzindo leiomiomas. Atinge preferencialmente mulheres em idade
fértil, surgindo raramente em fase pós-menopáusica.
O diagnóstico diferencial com carcinomatose peritoneal ou neoplasia maligna intra-abdominal disseminada é difícil de realizar
radiologicamente, sendo efectuado habitualmente através de biópsia e exame histológico
A partir de um caso clínico de uma mulher com LPD, os autores fazem uma revisão dos aspectos clínicos, anátomo-patológicos e
radiológicos desta entidade.
The Leiomyomatosis Peritonealis Disseminata (LPD) is an uncommon disease, often asymptomatic, characterized by multiple peritoneal or subperitoneal nodules corresponding to leiomyomas. Primarily affects women of reproductive age, affecting posmenopausal women rarely. Differential diagnosis of carcinomatosis peritonealis or abdominal disseminated malignancy it is a very difficult diagnosis and only biopsy and histological analysis can reveal the underlying disease. The authors present a case of a woman with LPD and a revision of the clinical, pathological and imaging features of this entity is also done.
The Leiomyomatosis Peritonealis Disseminata (LPD) is an uncommon disease, often asymptomatic, characterized by multiple peritoneal or subperitoneal nodules corresponding to leiomyomas. Primarily affects women of reproductive age, affecting posmenopausal women rarely. Differential diagnosis of carcinomatosis peritonealis or abdominal disseminated malignancy it is a very difficult diagnosis and only biopsy and histological analysis can reveal the underlying disease. The authors present a case of a woman with LPD and a revision of the clinical, pathological and imaging features of this entity is also done.
Description
Keywords
Leiomiomatose peritoneal disseminada Leiomioma Leiomyomatosis peritonealis disseminata Leiomyoma
Citation
Pedro Ferreira; Teresa Margarida Cunha. Leiomyomatosis Peritonealis Disseminata – Review of the Clinical and Imagiological Features Based on a Case Report, Acta Radiológica Portuguesa, 19, 73, 67-70, 2007.