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Incomplete Shone’s complex: adult age diagnosis

2017Journal article Open access
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dc.contributor.authorRodrigues, Ricardo C.
dc.contributor.authorCorreia, André
dc.contributor.authorSerrão, Gomes
dc.contributor.authorFaria, Paula
dc.contributor.authorGomes, Susana
dc.contributor.authorPereira, Décio
dc.date.accessioned2020-09-24T15:03:02Z
dc.date.available2020-09-24T15:03:02Z
dc.date.issued2017
dc.description.abstractA 25-year-old male with previous history of heart surgery was referred for a control echocardiogram. He had been operated when he was 5 years old for reparation of aortic coarctation and the excision of a subaortic membrane, and was then lost to follow-up. No other changes were detected previously or during surgery. The patient was clinically stable without medication and the physical exam was unremarkable. The echocardiogram showed normal left ventricular function, but bicuspid aortic valve (figure 1 A), conditioning mild aortic stenosis, and a parachute mitral valve (figure 1 B, C) with single papillary muscle (figure 1 D, E – arrow) were present, with slight increase in transmitral velocity and mild regurgitation. No residual coarctation was present. Shone’s complex is a rare congenital heart disease consisting of several levels of left-sided obstructive lesions including supravalvar mitral ring, parachute mitral valve subaortic stenosis and coarctation of aorta, being classified as complete (if all levels are present) or incomplete (if only 2 or 3 lesions are present). Our patient had a previous surgical intervention and no correction was made for two undiagnosed lesions. Furthermore, the main critical problem associated with this condition appears to be mitral valve obstruction which was not significant in our patient. A conservative approach was decided and at 3-year follow-up no events occurred. This case highlights the importance of exhaustive preoperative echocardiographic evaluation and reminds us that, in the presence of two-levels of left-side cavities obstruction, other possible related anatomical lesions must be excluded.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.doi10.1080/00015385.2017.1281529pt_PT
dc.identifier.issn0001-5385 (Print)
dc.identifier.issn0373-7934 (Online
dc.identifier.urihttp://hdl.handle.net/10400.26/33420
dc.language.isoengpt_PT
dc.publisherTaylor & Francispt_PT
dc.relation.publisherversionhttp://www.tandfonline.com/loi/tacd20pt_PT
dc.subjectAdultpt_PT
dc.subjectAortic Coarctationpt_PT
dc.subjectAortic Valvept_PT
dc.subjectEchocardiographypt_PT
dc.subjectHeart Defects, Congenitalpt_PT
dc.subjectHumanspt_PT
dc.subjectMalept_PT
dc.subjectMitral Valvept_PT
dc.subjectAbnormalities, Multiplept_PT
dc.subjectDelayed Diagnosispt_PT
dc.subjectPortugalpt_PT
dc.subjectMadeira Islandpt_PT
dc.titleIncomplete Shone’s complex: adult age diagnosispt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.endPage86pt_PT
oaire.citation.issue1pt_PT
oaire.citation.startPage85pt_PT
oaire.citation.titleActa Cardiologicapt_PT
oaire.citation.volume72pt_PT
person.familyNameRodrigues
person.givenNameRicardo C.
person.identifier.orcid0000-0002-5115-6991
person.identifier.scopus-author-id57189234203
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT
relation.isAuthorOfPublication74403bd2-294e-4cd0-8156-d9a6f622da50
relation.isAuthorOfPublication.latestForDiscovery74403bd2-294e-4cd0-8156-d9a6f622da50

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