Duarte, AFAlpuim Costa, DCaçador, NBoavida, AMAfonso, AMVilares, MDevoto, Martin2021-08-082021-08-082021Orbit . 2021 Mar 22;1-6. doi: 10.1080/01676830.2021.1901293.http://hdl.handle.net/10400.26/37287Epithelial tumors of the lacrimal gland are rare and usually develop in the orbital lobe. We report the exceedingly rare occurrence of a primary adenoid cystic carcinoma in the palpebral lobe of the lacrimal gland. A 26-year-old female was referred for evaluation of a gradually enlarging mass in the lateral upper eyelid, previously diagnosed as a chalazion. Computed tomography revealed a heterogeneous round lesion anterior to the orbital rim. Excisional biopsy was compatible with an adenoid cystic carcinoma. After excluding distant metastasis, and as the patient refused adjuvant radiotherapy, a second surgical procedure, with wide local excision, was indicated. Follow-up showed no recurrence. This case highlights the importance of performing a thorough clinical examination when diagnosing any lateral upper eyelid mass. A high index of suspicion for malignant tumors of the lacrimal gland should always be maintained, and a complete excision with histological analysis should be preferred whenever possible.engCarcinoma Adenoide QuísticoNeoplasias dos OlhosNeoplasias da OrbitaCarcinoma, Adenoid CysticEye NeoplasmsOrbital Neoplasmsjournal article10.1080/01676830.2021.1901293