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|Title: ||Adult diagnosis of Swyer-James-MacLeod syndrome: a case report|
|Authors: ||Capela, C|
|Keywords: ||Síndrome de Swyer-James-MacLeod|
|Issue Date: ||2011|
|Publisher: ||BioMed Central|
|Citation: ||J Med Case Reports. 2011;5:2.|
Swyer-James-MacLeod syndrome or unilateral hyperlucent lung syndrome is a rare entity associated with postinfectious bronchiolitis obliterans occurring in childhood. It is characterized by hypoplasia and/or agenesis of the pulmonary arteries resulting in pulmonary parenchyma hypoperfusion.
Here we report the case of a 53-year-old Caucasian woman with Swyer-James-MacLeod syndrome found in the differential diagnosis workup for a new onset of heart failure, secondary to pulmonary arterial hypertension complicated by a patent ductus arteriosus.
Typically, this disorder is diagnosed in childhood after evaluation for recurrent respiratory infections, but sometimes an indolent course means diagnosis is not made until adulthood.|
|Peer Reviewed: ||yes|
|Appears in Collections:||MED INT - Artigos|
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